Where does Angiomatoid fibrous histiocytoma occur?
Angiomatoid fibrous histiocytoma is an uncommon, low-grade malignant soft tissue tumor of uncertain histogenesis. It most commonly occurs in the deep dermis or subcutis of the extremities in children and young adults.
Is Angiomatoid fibrous histiocytoma fatal?
Angiomatoid fibrous histiocytoma (AFH) is a rare soft tissue tumor that has been associated with EWSR1-CREB1 gene fusion. Outcome in patients with unresectable distant metastases is generally fatal.
How common is Angiomatoid fibrous histiocytoma?
Angiomatoid fibrous histiocytoma (AFH) is a rare soft-tissue tumor with intermediate malignant potential and a median age of presentation of 14 years. It accounts for approximately 0.3% of soft-tissue neoplasms.
What is a Histiocytoma when found in humans?
A malignant fibrous histiocytoma is a type of cancerous tumor that can start in either bone or, most often, in the soft tissues that connect, support or surround organs and other body parts.
What is atypical fibrous histiocytoma?
Atypical fibrous histiocytoma is a distinctive variant of cutaneous fibrous histiocytoma, which is often mistaken histologically for sarcoma and which have a tendency to recur locally and a capacity to metastasize, although very rarely.
How many people get Angiomatoid fibrous histiocytoma?
Angiomatoid fibrous histiocytoma is a rare soft tissue tumor of low-grade malignancy that usually occurs in children and young adults. Eighty-eight percent of patients are 30 years of age or younger. Enzinger in 1979 first designated the tumor as angiomatoid malignant fibrous histiocytoma….Soft Tissues: Angiomatoid fibrous histiocytoma.
| Hybrid Gene | |
|---|---|
| Note | FUS/ATF-1 |
Is Angiomatoid fibrous histiocytoma rare?
Angiomatoid fibrous histiocytoma (AFH) is a rare soft tissue tumor most commonly occurring in children, adolescents, and young adults. Clinically and radiographically the lesion is easily confused with a hematoma, soft tissue hemangioma, or malignant fibrous histiocytoma.